Truncus Arteriosus: Pulmonary Vascular Disease Screening
Author : N.G. Liman, G.M. Harimurti
Upload Date : 19-04-2018
Truncus arteriosus accounts for 1% of all congenital heart diseases. The characteristic of truncus arteriosus is the defect of the aorticopulmonary septum so that the common trunk originates from the heart and branches to the systemic, lung, and coronary vessels with variations of morphology. Pulmonary vascular disease is a risk factor for truncus arteriosus surgery. Therefore, truncus arteriosus surgery is usually performed early in infancy before irreversible pulmonary vascular disease occurs. Patient was a six-month-old boy, with Ross II heart failure in type I truncus arteriosus, mild truncal regurgitation, and large perimembranous ventricular septal defect. Screening for pulmonary vascular disease can be done by catheterization and pulmonary vascular resistance formula. In this case, pulmonary vascular resistance was calculated using the formula and the patient's pulmonary vascular resistance obtained with oxygen nasal cannula administration was 4.70 Wood units/m2. This pulmonary vascular resistance level indicates that there is no pulmonary vascular disease in the patient and the patient is a candidate for surgical management.
KEYWORDS : truncus arteriosus; embryology; pulmonary vascular disease