Advanced

Double-Outlet Right Ventricle with Dextrocardia in a One-year-old girl: A Case Report

Author : D. Hertriwibowo, K. N. Hapsara, F. S. Hasibuan
Upload Date : 19-04-2018

Background: Double outlet right ventricle (DORV) is a heterogeneous collection of lesions that share one morphologic feature, namely that both the aorta and the pulmonary artery arise from the right ventricle. It is a very rare case and only comprises about 1-1,5% of all congenital heart diseases.

Methods: We report a rare case of DORV with dextrocardia in a one-year-old girl.

Results: A one-year-old girl, presented to pediatric outpatient clinic of  Dr. R. Koesma General Hospital, with chief complaint of cough followed by dyspnea. She had history of recurrent cough, breathlessness and cyanosis that occurred when she was crying. Upon examination, no cyanosis was found. Harsh systolic murmur was heard on the left sternal border. Chest x-ray revealed dextrocardia and decreased pulmonary vascular markings. The patient was diagnosed with congenital heart disease (CHD) and then consulted to cardiologist for echocardiography evaluation to confirm the diagnosis.

2D echocardiography showed the following findings: situs solitus; dextrocardia mirror image; critical pulmonary stenosis with VA connections discordance; Aorta overriding more than 50%, ventricular septal defect malalignment; PDA with left to right shunt and pulmonary artery arise from the right ventricle suspecting DORV.

The patient was then referred to Dr. Soetomo Hospital for further evaluation and treatment.

Conclusion: Despite the rarity of DORV, physician needs to be aware of this disease, as the clinical presentation can be vary. This congenital heart disease is almost always associated with VSD, and in some cases, it can also be accompanied by other cardiac anomaly, which will later affect the clinical presentation.

We can see in this case report that echocardiography plays an important role for diagnosing this disease with all the cardiac anomaly, thus helps determining the right treatment and intervention for the patient.

KEYWORDS : DORV, echocardiography, congenital heart disease, one-year-old girl.


Save Item
Download
Similar Articles

The Differences of Echocardiographic Features between Mitral Regurgitation Patients with Sinus Rhythm and Atrial Fibrillation (V. B Kusmanto, A. M. Soesanto, E. Rudiktyo, R. Ariani, B. R. M. A. S. Kuncoro)

Relation between Adiponektin Level with The Right Ventricular Function in Adult Uncorrected Secundum Atrial Septal Defect Patient(D. Aji,W. Himawan ,D. W. Anggraini , A. B. Hartopo , L. K. Dinarti)

Pattern of Rheumatic Heart Disease: An Echocardiographic Study (G. Aditya, T. N. P. Adityaputra, I. B. R.Wibhuti, K. B.Nadha)

Pregnancy Outcomes in Women with Uncorrected Congenital Heart Disease: A Single-Centre Experience(A. Wardhani, A. Yudanto, M.B.A. Pramono, Y. Herry)

The Difference on Strain and Strain Rate Parameter of Left Ventricle Function Between Controlled Hypertension and Uncontrolled Hypertension(M. Reza, B. R. M. A. Soeryo, R. Soerarso)

Left Ventricular Dimension and Ejection Fraction Values by Echocardiography in Adolescents: An Epidemiology Study in Bali, Indonesia(L. O. S. Suastika, I. B. R. Wibhuti, K. B. Nadha, M. Chowdhury, J. Chowdhury, K. Olejnik, E. Bouman,)

Correlation between Estimated Right Ventricular Systolic Pressure and Tricuspid Annular Plane Systolic Excursion to Perinatal Outcome in Pregnancy with Acyanotic Congenital Heart Disease(A. Pudjiastuti, A.A. Asrial, A. Sariningrum, L. Raharjoyo, Y.A.B.M. Aruman, M.A. Nugroho, Y. Herry)

Diagnostic and Management Approach of Patients with Coronary Artery Fistula: Case Series(N.I. Gayatri, O. Lilyasari, P.S. Roebiono, A.U. Rahayoe, I. Sakijan, R. Prakoso, Y. Kurniawati, G.M.)

A Rare Case of Multiple Intracardiac Tumors in Pediatric(B. Saunders, I. Sulistyorini I. Mappangara, Y. Patimang, B. Iskandar)

Role of Supporting Examination in Investigating Non Specific Chest Pain to Diagnose Thoracic Aorta Aneurysm in Rural Setting: A Case Report(M. Abduh, H. Nainggolan, J. Endang)

Role of Trans Thoracal Echocardiography (TTE) in Assessing Aortic Abnormalities in Patient with suspected Marfan Syndrome: A Case Report(A.W. Sari, B. Nadha, R. Wibhuti)

Copyrights 2018 ASMIHA | Managed by Indonesia Medical Event (IME)